周围型原始神经外胚层肿瘤患儿的CT影像学特征分析

doi:10.3969/j.issn.1671-7171.2023.02.010

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摘要【目的】探讨周围型原始神经外胚层肿瘤(Peripheral primitive neuroectodemal tumor,pPNET)患儿的CT影像学特征。【方法】回顾性分析经组织病理学检查确诊的11例pPNET患儿的CT影像学资料,所有患儿均行CT平扫及增强检查,分析肿瘤发病部位、CT影像学特征及病理学检查结果。【结果】11例pPNET患儿中,肿瘤发生于颈部2例,发生于肩背部、胸壁、肾上腺、腹膜后、臀部、大腿,前臂,肱骨及股骨各1例。肿瘤发生于骨外组织者表现为较大的软组织肿块,边界不清,密度不均匀,钙化(1例),出血(2例)少见,增强扫描多呈中重度强化(7例),内部见小血管影。2例发生于四肢骨的pPNET患儿表现为骨质破坏和软组织肿块,均未见肿瘤骨,1例无骨膜反应,1例骨皮质有中断伴有少量骨膜反应。软组织肿块呈明显强化。【结论】pPNET患儿CT影像学表现缺乏特异性,难于与其他骨及软组织的恶性肿瘤鉴别,临床主要依靠病理检查确诊。

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	李春旺
	汤静

关键词 ：神经外胚瘤,原始,外周/影像诊断, 体层摄影术,螺旋计算机

Abstract：【Objective】To investigate the CT imaging features of peripheral primitive neuroectodermal tumor (pPNET) in children. 【Methods】 The CT imaging data of 11 patients with pPNET confirmed by histopathological examination were retrospectively analyzed. All patients underwent plain and enhanced CT scanning,and the tumor location. CT imaging features and pathological examination results were analyzed. 【Results】Of the 11 children with pPNET,2 tumors occurred in the neck ,and it also occurred in shoulder and back,chest wall,adrenal gland,retroperitoneum,buttock,thigh,forearm,humerus and femur in 1 case respectively. The tumor occurred outside the bone and was characterized by large soft tissue mass with unclear boundary and uneven density,calcification (1 case) and hemorrhage (2 cases).The enhancement scan showed moderate and severe enhancement (7 cases),with small vessel shadow inside. Two children with pPNET occurred in the bones of limbs showed bone destruction and soft tissue mass,and no tumor bone was found; There was no periosteal reaction in 1 case,and the bone cortex was interrupted in 1 case with a small amount of periosteal reaction. The soft tissue mass showed obvious enhancement. 【Conclusion】 The CT imaging findings of children with pPNET are lack of specificity and difficult to differentiate from other malignant tumors of bone and soft tissue. The clinical diagnosis mainly depends on pathological examination.

Key words： Neuroectodermal Tumors, Primitive, Peripheral/DG Tomography, Spiral Computed

收稿日期: 2022-11-29

中图分类号:

R739.43

基金资助:湖南省卫健委课题项目(202209012654)

引用本文:

李春旺, 汤静. 周围型原始神经外胚层肿瘤患儿的CT影像学特征分析[J]. 医学临床研究, 2023, 40(2): 195-197.
LI Chun-wang, TANG Jing. CT Imaging Characteristics of Peripheral Primitive Neuroectodermal Tumors in Children. JOURNAL OF CLINICAL RESEARCH, 2023, 40(2): 195-197.

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http://journal07.magtech.org.cn/yxlcyj/CN/10.3969/j.issn.1671-7171.2023.02.010 或 http://journal07.magtech.org.cn/yxlcyj/CN/Y2023/V40/I2/195

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