儿童胸膜肺母细胞瘤CT影像学特征分析<sup>*</sup>

doi:10.3969/j.issn.1671-7171.2024.10.004

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Abstract 【Objective】To analyze the CT imaging features of pleuropulmonary blastoma (PPB) in children. 【Methods】Clinical and CT imaging data of 10 children with PPB confirmed by puncture biopsy or surgical pathology admitted to the Department of Radiology of Hunan Children's Hospital from August 2016 to July 2022 were retrospectively analyzed. All cases underwent plain and enhanced CT scan. Among them, 5 were male and 5 were female. The ages ranged from 1 year 2 months to 4 years 11 months, with a median age of 3 years 2 months. The main symptoms of non-specific respiratory tract infection were fever, cough, shortness of breath and chest pain. 【Results】All the 10 cases were single, 6 cases on the right side and 4 cases on the left side. Among the 10 cases, 1 case was type Ⅰ, 2 cases were type Ⅱ, and 7 cases were type Ⅲ. In 8 cases, the masses were located in the periphery of the lung and pressed the lung tissue and mediastinum to the healthy side, 1 in the lung lobe and 1 around the lung hilum. The tumors were all larger than 6.5 cm in diameter, and in 6 cases, the mass occupied almost half of the thoracic cavity. One case was complicated with left renal cystic tumor. CT findings: Type Ⅰ presented as a multilocular cystic mass filled with fluid and containing a small amount of gas. Type Ⅱ was a solid cystic mass with soft tissue density in the plain scan, uneven mild enhancement, and no enhancement in the cystic mass. Type Ⅲ was a pure solid mass with clear boundaries, uneven enhancement, and multiple tumor-nourishing vessels. Rib destruction and mediastinal lymph node enlargement were not observed in all cases, with or without a small amount of pleural effusion, and only 2 cases had a small amount of calcification. 【Conclusion】In children aged 2 to 4 years old, CT found a huge mass close to the chest wall on one side of the chest, but no obvious involvement in the chest wall and no bone destruction of the ribs. The possibility of PPB should be considered first.

Key words： Lung Neoplasms/DG Pleural Neoplasms/DG Child Tomography, Spiral Computed

Received: 13 May 2024

PACS:

R734.2

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	LI Chunwang
	LI Shuming
	TANG Jing

Cite this article:

LI Chunwang,LI Shuming,TANG Jing. CT Imaging Features of Pleuropulmonary Blastoma in Children[J]. JOURNAL OF CLINICAL RESEARCH, 2024, 41(10): 1468-1471.

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http://journal07.magtech.org.cn/yxlcyj/EN/10.3969/j.issn.1671-7171.2024.10.004 OR http://journal07.magtech.org.cn/yxlcyj/EN/Y2024/V41/I10/1468

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