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| CT Imaging Characteristics of Peripheral Primitive Neuroectodermal Tumors in Children |
| LI Chun-wang, TANG Jing |
| Department of Radiology,Hunan Children's Hospital,Changsha Hunan 410007 |
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Abstract 【Objective】To investigate the CT imaging features of peripheral primitive neuroectodermal tumor (pPNET) in children. 【Methods】 The CT imaging data of 11 patients with pPNET confirmed by histopathological examination were retrospectively analyzed. All patients underwent plain and enhanced CT scanning,and the tumor location. CT imaging features and pathological examination results were analyzed. 【Results】Of the 11 children with pPNET,2 tumors occurred in the neck ,and it also occurred in shoulder and back,chest wall,adrenal gland,retroperitoneum,buttock,thigh,forearm,humerus and femur in 1 case respectively. The tumor occurred outside the bone and was characterized by large soft tissue mass with unclear boundary and uneven density,calcification (1 case) and hemorrhage (2 cases).The enhancement scan showed moderate and severe enhancement (7 cases),with small vessel shadow inside. Two children with pPNET occurred in the bones of limbs showed bone destruction and soft tissue mass,and no tumor bone was found; There was no periosteal reaction in 1 case,and the bone cortex was interrupted in 1 case with a small amount of periosteal reaction. The soft tissue mass showed obvious enhancement. 【Conclusion】 The CT imaging findings of children with pPNET are lack of specificity and difficult to differentiate from other malignant tumors of bone and soft tissue. The clinical diagnosis mainly depends on pathological examination.
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Received: 29 November 2022
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2023, Vol. 40 
